Nerve conduction studies (NCS) | |||||
---|---|---|---|---|---|
Variables | Normal (N = 35) | Abnormal (N = 12) | P | ||
N | % | N | % | ||
Sex Male Female | 24 11 | 82.6 68.8 | 5 5 | 17.4 31.2 | 0.449 |
Age (years) Mean ± SD | 18.92 ± 1.33 | 20.10 ± 1.10 | 0.008 | ||
Age < 16 years ≥ 16 years | 0 35 | 0 100 | 0 12 | 0 100 | 1.000 |
Duration of disease (years) Mean ± SD | 17.28 ± 1.84 | 18.30 ± 1.49 | 0.090 | ||
Transfusion frequency < 10 times/year ≥ 10 times/year | 1 34 | 100 73.9 | 0 12 | 0 26.1 | 1.000 |
Splenomegaly No Yes | 19 16 | 76 72.7 | 6 6 | 24 27.3 | 0.066 |
Splenectomy No Yes | 28 7 | 82.4 53.8 | 6 6 | 17.6 46.2 | 0.156 |
Hepatomegaly No Yes | 6 29 | 50 82.9 | 50 17.1 | 52.4 44.3 | 1.000 |
Iron chelation therapy Deferoxamine Deferasirox Deferiprone Combined | 13 13 4 5 | 72.2 86.7 66.7 63 | 5 2 2 3 | 27.8 13.3 33.3 37 | 0.414 |