Table 1 Baseline characteristics of the studied patients

Age (years; mean ± SD)

6.58 ± 4.16

Range

1–17

Gender (% male)

28 (56.0%)

Consanguinity

24 (48.0%)

Socioeconomic status

 Middle

16 (32.0%)

 Low

34 (68.0%)

Body mass index (kg/m²)

14.48 ± 2.55

Range

10.9–19.8

Etiology of bronchiectasis

 • Cystic fibrosis

30 (60%)

 • Post-infective

12 (24%)

 • Allergic bronchopulmonary aspergillosis

4 (8%)

 • Kartagener syndrome

2 (4%)

 • Idiopathic

2 (4%)

FEV1% predicted

 Mean ± SD

70.00 ± 26.51

 Range

45–110

Chronic infection, n (%)

 P. aeruginosa

22 (44.0%)

 MRSA^a

18 (36.0%)

 Streptococcus pneumoniae

4 (8%)

 Klebsiella

2 (4%)

 Escherichia coli

2 (4%)

 Enterococci

2 (4%)

 Median sputum neutrophil elastase (ng/ml) (IQR)

30 (24–64)

Range

6–140

Bronchiectasis severity index (mean ± SD)

10.36 ± 2.80

Range

6–16

Median FACED score (IQR)

2 (1–2)

Range

0–5

Modified Reiff score (mean ± SD)

6.72 ± 1.26

Range

3–8

Bhalla score (mean ± SD)

16.44 ± 3.73

Range

12–24

Cough severity score (mean ± SD)

25.60 ± 7.31

Range

14–38

Median exacerbations last year (IQR)

2 (1–3)

Range

1–6

CFTR genotype

 Homozygous F508del

6 (20.0%)

 Heterozygous F508del

4 (13.3%)

 Other/others

14(46.6%)