From: Pulmonary dysfunction in children with Cystinosis: single center study, original article
 | chest wall shape | P value | |||
---|---|---|---|---|---|
Normal | Barrel | ||||
Mean ± SD | Median / range | Mean ± SD | Median / range | ||
R5 | 136.42 ± 10.22 | 137.80 (123.90_151.00) | 139.89 ± 22.39 | 145.05 (102.10_163.20) | 0.513 |
R20 | 132.32 ± 21.72 | 129.20 (106.30_165.00) | 116.53 ± 15.92 | 118.80 (94.30_137.00) | 0.206 |
X5 | 91.10 ± 30.77 | 86.20 (51.50_132.50) | 41.04 ± 59.55 | 40.00 (−89.40_114.90) | 0.099 |
Fres | 39.51 ± 9.94 | 44.95 (22.92_ 46.94) | 38.47 ± 16.30 | 39.30 (4.11_58.13) | 0.768 |
Ax | 4.01 ± 2.35 | 3.32 (1.60_7.01) | 4.52 ± 1.69 | 4.31 (1.88_7.01) | 0.594 |
FEV1 | 93.65 ± 6.15 | 93.65 (89.30_98.) | 77.38 ± 29.01 | 70.60 (53.70_114.60) | 0.533 |
FVC | 90.90 ± 1.27 | 90.90 (90.00_91.80) | 68.30 ± 25.10 | 62.75 (47.50_100.20) | 0.533 |
FEV1% | 107 | 107 | 113.15 ± 2.27 | 113.80 (110 _115) | 0.400 |
FEF25% | 111.05 ± 37.55 | 111.05 (84.50_137.60) | 90.75 ± 49.29 | 76.85 (52.80_156.50) | 0.800 |
FEF50% | 66.70 ± 32.10 | 66.70 (44.00_89.40) | 73.03 ± 25.84 | 62.10 (56.80_111.10) | 1.000 |
FEF75% | 82.45 ± 20.58 | 82.45 (67.90_97.00) | 60.15 ± 12.09 | 56.00 (50.70_77.90) | 0.267 |