Clinical Parameters | Score | ||||
---|---|---|---|---|---|
1 | 2 | 3 | 4 | 5 | |
Vaso-occlusive crisis/year | 0–1 | >1–3 | >3–5 | >5–8 | >8–12 |
Hospitalization due to severe vaso-occlusive crises/year | 0 | 1–2 | 3–4 | >5 |  |
Blood transfusion/year | 0 | 1–2 | 3–5 | >5 |  |
Acute chest syndrome | No | Yes | Â | Â | Â |
Stroke | No | Yes | Â | Â | Â |
Avascular necrosis of femur | No | Yes | Â | Â | Â |
Spleen size | Not palpable | 3–4 cm | 5–7 cm |  |  |